兔抗FBN1多克隆抗体

Background:

This gene encodes a member of the fibrillin family. The encoded protein is a large, extracellular matrix glycoprotein that serve as a structural component of 10-12 nm calcium-binding microfibrils. These microfibrils provide force bearing structural support in elastic and nonelastic connective tissue throughout the body. Mutations in this gene are associated with Marfan syndrome, isolated ectopia lentis, autosomal dominant Weill-Marchesani syndrome, MASS syndrome, and Shprintzen-Goldberg craniosynostosis syndrome.

Applications:

ELISA, IHC

Name of antibody:

FBN1

Immunogen:

Synthetic peptide of human FBN1

Full name:

fibrillin 1

Synonyms：

FBN, SGS, WMS, MASS, MFS1, OCTD, SSKS, WMS2, ACMICD, ECTOL1, GPHYSD2

SwissProt:

P35555

ELISA Recommended dilution:

1000-5000

IHC positive control:

Human thyroid cancer

IHC Recommend dilution:

50-200